This question describes I-cell disease (inclusion cell disease/mucolipidosis type II). You can tell because there is mixed accumulation of junk forming the inclusion bodies. Other lysosomal storage diseases have accumulation of one type of substance.
Essentially, there is a defect in defect in the enzyme N-acetylglucosaminyl-1-phosphotransferase.
This means the mannose-6-phosphate tag cannot be added to proteins. Without this tag, proteins are incorrectly sent to the extracellular space rather than delivered to lysosomes.